NAGLU (54-G)

mouse

抗-NAGLU 抗体 54-G 是小鼠单克隆 IgG2a (kappa轻链)，NAGLU抗体，规格为100 µg/ml raised against a partial recombinant protein mapping within amino acids 644-743 of NAGLU of human origin 推荐用于 mouse, rat 和 human 来源的NAGLU WB 和 IP检测 关于如何获取NAGLU (54-G): sc-130383的免费10 µg小样，联系我们技术服务部门 (或者您当地的代理商)了解详情。 目前，我们还没有完成NAGLU 抗体 (54-G)的首选二抗检测试剂的鉴定。这项工作正在进行中。 NAGLU Antibody (54-G) is a high quality monoclonal NAGLU antibody (also designated NAGLU antibody) suitable for the detection of the NAGLU protein of mouse, rat and human origin. NAGLU Antibody (54-G) is available as the non-conjugated anti-NAGLU antibody. NAGLU (N-acetyl-alpha-glucosaminidase), also known as NAG, UFHSD1, MPS3B or MPS-IIIB, is a 743 amino acid protein that exists as both a monomer and a homodimer. Expressed in ovary, liver, testis, prostate, lung, colon, kidney, spleen, placenta and peripheral blood leukocytes, NAGLU is involved in the degradation of heparan sulfate (HS), specifically functioning to catalyze the hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in the gene encoding NAGLU are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. MPS-IIIB is an autosomal recessive disorder in which the body fails to degrade HS, leading to an accumulation of HS in lysosomes and urine and resulting in mental deterioration and, ultimately, death.For Research Use Only. Not Intended for Diagnostic or Therapeutic Use.

Replacement monoclonal antibody for: sc-168707, sc-168708.

IGG-免疫球蛋白G型抗体

HumanNAGLU

4669;27419