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BLOC1S3, CT (BLOC1S3, BLOS3, Biogenesis of lysosome-related organelles complex 1 subunit 3)

产品介绍
产品介绍
产品信息
纯化方式
Affinity Purified
Purified by Protein A affinity chromatography.

抗原名称
biogenesis of lysosome-related organelles complex 1 subunit 3

免疫原
BLOC1S3 antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 176-202 amino acids from the C-terminal region of human BLOC1S3.

商品描述
This gene encodes a protein that is a component of the BLOC1 multi-subunit protein complex. This complex is necessary for the biogenesis of specialized organelles of the endosomal-lysosomal system, including platelet dense granules and melanosomes. Mutations in this gene cause Hermansky-Pudlak syndrome 8, a disease characterized by lysosomal storage defects, bleeding due to platelet storage pool deficiency, and oculocutaneous albinism.

形式
Supplied as a liquid in PBS, pH 7.2, 0.09% sodium azide.

产品类型
Polyclonal

应用
实验应用
ELISA (EL/EIA), Western Blot (WB)

反应种属
Human

背景
别名
Anti -BLOC1S3, CT (BLOC1S3, BLOS3, Biogenesis of lysosome-related organelles complex 1 subunit 3)

制备和贮存
保存方式
May be stored at 4 degree C for short-term only. Aliquot to avoid repeated freezing and thawing. Store at -20 degree C. Aliquots are stable for 12 months. For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap.
数据库链接
NCBI
388552

UniProt ID
Q6QNY0
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